REVIEW PAPER
HEARING DISORDERS AND AUDITORY SPEECH PROCESSING DIFFICULTIES IN ADULTS WITH DOWN SYNDROME: A REVIEW OF THE LITERATURE
 
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1
Radboud University Nijmegen Medical Centre – Department of Medical Psychology, Child Neurology Centre and NCEBP
2
University of Groningen, Centre for Language and Cognition (CLCG)
3
Radboud University Nijmegen Medical Centre – Department of Primary and Community Care
4
Radboud University Nijmegen Medical Centre – Department of Otorhinolaryngology and Donders Institute for Brain, Cognition and Behaviour
CORRESPONDING AUTHOR
Marjolein C. Coppens-Hofman   

Marjolein C. Coppens-Hofman, Radboud University Nijmegen Medical Centre – Department of Medical Psychology, Child Neurology Centre and NCEBP, e-mail: M.Coppens@mps.umcn.nl
Publication date: 2020-04-20
 
J Hear Sci 2011;1(3):11–17
 
ABSTRACT
A literature search was performed to review published articles on hearing disorders, auditory perceptual disorders and shortterm memory in adults with Down syndrome. The aim of the review was to identify factors determining impairments in these domains in order to improve care. A high prevalence was reported for hearing disorders in adults with Down syndrome. The syndrome appears to be an important determinant of communication difficulties, and it appears that auditory memory is related to speech and language skills. However, only a few studies have been published on diagnosis and intervention. The effects of hearing aids use are not always satisfying, but recent developments show promising alternatives. Suggestions are formulated to guide new research that could lead to better care concerning hearing difficulties.
 
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